Breneman, Gifford, and DeJong (2012) report best practices for audiological management of a child with auditory neuropathy spectrum disorder (ANSD) have yet to be developed. They evaluated 70 pediatric subjects, 35 of whom were diagnosed (15 females) with ANSD and 35 of whom were diagnosed (18 females) with sensorineural hearing loss (SNHL). The two groups were matched with respect to age at initial cochlear implant (CI) evaluation and months of CI use at test. The mean age at CI activation for the ANSD group was 38.5 months and 39.9 for the SNHL group. By the time testing was accomplished, the mean months of CI use was 71 months for each group.
The authors report that “many children with ANSD can clearly benefit from cochlear implantation…” Further, 32 of 35 children with ANSD achieved some open-set word recognition ability. Likewise, matched-pairs analysis of speech perception measures indicated no significant difference between the ANSD and the SNHL groups on any assessed measures. The authors recommend CIs be considered for children with ANSD and normal auditory nerves, who demonstrate poor progress with hearing aid amplification.
For More Information, References, and Recommendations
Breneman AI, Gifford RJ, DeJong MD. (2012) Cochlear Implantation in Children with Auditory Neuropathy Spectrum Disorder – Long Term Outcomes. Journal of the American Academy of Audiology (JAAA) 23(5):5–17.
Roche JP, Huang BY, Castillo M, Bassim MK, Adunka OF, Buchman CA. (2010) Imaging Characteristics of Children with Auditory Neuropathy Spectrum Disorder. Otology & Neurotology 31(5):780–788.
Roush PA. (2011) Children with Auditory Neuropathy Spectrum Disorder. In the "Comprehensive Handbook of Pediatric Audiology." Eds Richard Seewald and Anne Marie Tharpe. Plural Publishing, San Diego, CA,734–750.
Roush P, Frymark T, Venediktov R, Wang B. (2011) Audiologic Management of Auditory Neuropathy Spectrum Disorder in Children – A systematic review of the Literature. American Journal of Audiology 20(December):159–170.
Spirakis SE. (2011) Auditory Neuropathy Spectrum Disorder and Hearing Aids: Re-Thinking Fitting Strategies. Hearing Review. October.
Teagle HFB, Roush PA, Woodard JS, Hatch DR, Zdanski CJ, Buss E, Buchman CA. (2010) Cochlear Implantation in Children with Auditory Neuropathy Spectrum Disorder. Ear & Hearing 31(3):325–335